Susac syndrome as an example of a rare vasculopathy.
نویسندگان
چکیده
Susac syndrome is a rare vasculopathy affecting small vessels of the brain, the retina and the cochlea. The pathogenesis of this syndrome is unknown. It is characterized by a triad of clinical symptoms, i.e. encephalopathy, visual disorders and hearing disorders. The aim of this work was to review available data about the clinical course, diagnosis and treatment of Susac syndrome.
منابع مشابه
Evaluation of Retinal Changes Using Optical Coherence Tomography in a Pediatric Case of Susac Syndrome
Susac syndrome is a rare occlusive vasculopathy affecting the retina, inner ear and brain. The cause is unknown, although it generally affects young women. This syndrome can be difficult to diagnose because its signs can only be revealed by detailed examination. These signs are not always concomitant, but may appear at different times. This report describes a pediatric case who was diagnosed wi...
متن کاملRetinal vasculitis in Susac syndrome: case report.
A 29 year old male was admitted at the emergency room suffering from gradually worsening headache followed by nausea. In the hospital patient presented with lethargy, reduction of consciousness level and bilateral hypoacusis. Ophthalmic examination and fluorescein angiography showed retinal vasculitis. This finding was crucial to the diagnosis of Susac syndrome, a rare disease characterized by ...
متن کاملگزارش یک مورد سندروم نادر Susac از بخش نورولوژی بیمارستان امام خمینی، سال 1378
This syndrome is a very rare neurological presentation which was first reported by Susac in 1975, and usually involves the young women with triad of: (1) Visual loss due to occlusion of retinal artery branches. (2) Subacute encephalopathy with psychic manifestation, personality disorders, involvement of the cortico-spianal tracts, pseudo-bulbar, focal or generalized seizures and myoclonic jerks...
متن کاملCASE REPORT Susac Syndrome: Retinocochleocerebral Vasculopathy
Susac syndrome is a rare microangiopathy of cochlea, retina, and brain. We report a case of a 30-year-old man with Susac syndrome. The patient initially suffered from unilateral hearing loss associated with peripheral vestibular syndrome, and followed with recurrent arterial retinal occlusions and encephalopathy. The patient underwent clinical, laboratory, and neuroradiological examination. Lab...
متن کاملLetter to the Editor: Sneddon's Syndrome versus Susac Syndrome
Dear Editor, I read with interest the article titled “Acute central retinal artery occlusion associated with livedoid vasculopathy: a variant of Sneddon’s syndrome [1] and there may be a different diagnosis. Since a few cases of young patients have been identified with Susac syndrome with livedo, could this case represent a case of this disorder? Did the patient have an magnetic resonance imagi...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید
ثبت ناماگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید
ورودعنوان ژورنال:
- Polskie Archiwum Medycyny Wewnetrznej
دوره 119 1-2 شماره
صفحات -
تاریخ انتشار 2009